..., but patients with this syndrome are not known to have an increased risk of solid pseudopapillary neoplasms. Other rare, likely anecdotal associations include other neoplastic conditions (hairy cell leukemia, papillary thyroid carcinoma, neuroblastoma, mesothelioma, pancreatic intraductal papillary mucinous...

... is characterized by somatic gigantism, omphalocele, organomegaly including macroglossia, hemihypertrophy, adrenal cytomegaly, and an increased risk of embryonal neoplasms including Wilms tumor, hepatoblastoma, neuroblastoma, and rhabdomyosarcoma ( 30 ). BWS is caused by an assortment of epigenetic and genetic...

... are PanNETs, extrapancreatic neuroendocrine tumors in the esophagus ( 499 ), small bowel ( 500 ), kidney, and other sites can also produce VIP. VIP-producing neurogenic neoplasms have also been designated VIPomas; these include ganglioneuromas, ganglioneuroblastomas, neuroblastomas, and paragangliomas...

... in neuroendocrine tumors, but pancreatic ductal adenocarcinomas were negative ( 129 ). Another recent study evaluated 97 neuroendocrine tumors of various types (middle ear adenoma, paragangliomas, PitNET, medullary thyroid carcinoma, olfactory neuroblastoma, small cell carcinoma, large cell neuroendocrine carcinoma...

... neuroblastoma, adrenocortical carcinoma, and rhabdomyosarcoma, as well as many other tumors, both malignant and benign ( 762 ). This increased risk for neoplasia is concentrated in the first 8 years of life; tumor development is uncommon after this age. Individuals with uniparental disomy of 11p15.5 or gain...

... Urol   2000 ; 164 : 1709 - 10 . 26. Kushner   BH , Vogel   R , Hajdu   SI , Helson   L . Metastatic neuroblastoma and testicular involvement . Cancer   1985 ; 56 : 1730 - 2 . 27. Gupta   TD , Grabstald   H . Melanoma of the genitourinary tract . J Urol   1965 ; 93...

... detected in a rare melanotic neuroectodermal tumor of infancy: a case report . BMC Cancer   2016 ; 16 : 629 . 163. Calonge   WM , Heitor   F , Castro   LP , et al . Neonatal paratesticular neuroblastoma misdiagnosed as in utero torsion of testis . J Pediatr Hematol Oncol   2004 ; 26...

... carcinoma 3-4 Miscellaneous 1-2  Neuroblastoma  Ewing sarcoma/primitive neuro-ectodermal tumor (PNET)  Synovial sarcoma  Angiomyolipoma  Lymphoma  Other rare neoplasms Table 1-3 THREE MAIN CONGENITAL SYNDROMES ASSOCIATED WITH NEPHROBLASTOMA ^a Syndrome...

... by S-100 protein immunostaining. Occasional bizarre nuclei, such as seen in other neuroendocrine neoplasms, may be present. Rare examples of composite paraganglioma-ganglioneuroma and paraganglioma with neuroblastoma-like foci have been described ( 711 – 713 ). Mitotic figures are variable. Vascular...

...Table 11-2 DIFFERENTIAL DIAGNOSIS OF MALIGNANT SMALL ROUND CELL TUMORS IN BONE Ewing sarcoma Rhabdomyosarcoma Neuroblastoma (metastasis) Non-Hodgkin lymphoma/leukemia Small cell osteosarcoma Mesenchymal chondrosarcoma Poorly differentiated monophasic synovial sarcoma...

...-macrocystic subtype of renal cell carcinoma that is associated with the tuberous sclerosis complex ( 365 , 381 ), and is considered its sporadic counterpart. Some cases previously reported as “oncocytoid renal cell carcinoma after neuroblastoma” also have proven to be this entity ( 378 ). Gross Findings...

... and sarcoma can also metastasize to bone. In children, tumors that tend to spread to bone are neuroblastoma and rhabdomyosarcoma. Clinical Features . The skeleton is one of the most common sites for metastatic disease. Most patients with metastatic disease to bone have a known primary. Sometimes...

... conditions include myelodysplastic syndrome, acute leukemia, neuroblastoma, and sickle cell disease ( 115 – 117 ). The patients often have a history of myeloablative total body irradiation and have received alkylating agents and etoposide ( 115 – 117 ). The interval between transplantation...

... round cell tumor, but Ewing sarcoma has cytoplasmic glycogen and a more cohesive growth pattern, and less pleomorphic nuclei than lymphoma ( 52 ). Neuroblastoma may present with bony metastases but its tumor cells are pear-shaped or carrot-shaped, with denser chromatin than lymphoma...

..., the intravillous malignancy “invades” the villous stroma and even involves the intervillous space ( 110 ). The most common fetal malignancy involving the placenta is a leukemia, although solid tumors (most commonly neuroblastoma) and sarcomas have been reported (see Microscopic Variants) ( 111 , 111a ). FETAL...

..., pineoblastoma: the Flexner-Wintersteiner rosettes and fleurettes. The Homer Wright rosette of retinoblastoma is identical morphologically to its counterpart in conditions such as neuroblastoma. Flexner-Wintersteiner rosettes, the most typical type seen in retinoblastoma, are characterized by an empty center...

... undergoing extensive local excision, 1 had local recurrence and 2 died from disease ( 97 ). Three scrotal examples of Merkel cell carcinoma have been described ( 144 – 146 ). Cases of peripheral neuroectodermal tumors (PNET) and congenital neuroblastoma of the scrotum have also been reported ( 147...

... - 8 . 49. Oyama   K , Yamada   S , Usui   M , Kovacs   K . Sellar neuroblastoma mimicking pituitary adenoma . Pituitary   2005 ; 8 : 109 - 14 . 50. Lin   JH , Tsai   DH , Chiang   YH . A primary sellar esthesioneuroblastomas with unusual presentations: a case...